A Case of Linear and Whorled Nevoid Hypermelanosis with Intracranial Lipoma.

Song,  Tae Won; Yoo,  Byung Won; Lee,  Young Mock; Kang,  Du Cheol; Lee,  Joon Soo; Coe,  Chang Jun

Case Report

Journal of the Korean Child Neurology Society 2003;11(1):150-157.
Published online May 30, 2003.

A Case of Linear and Whorled Nevoid Hypermelanosis with Intracranial Lipoma.

Tae Won Song, Byung Won Yoo, Young Mock Lee, Du Cheol Kang, Joon Soo Lee, Chang Jun Coe

Department of Pediatrics, Institute of Handicapped Children, Yonsei University College of Medicine, Seoul, Korea. pedneu@yumc.yonsei.ac.kr

Abstract

Linear and whorled nevoid hypermelanosis(LWNH) is characterized by macules in streaks and whorls along Blaschko's lines, that are not preceded by inflammation. LWNH can present with various findings such as neurologic, musculoskeletal, ophthalmologic, facial and cardiac abnormalities. Intracranial lipoma is very rare condition, with an incidence of less than 1% of all intracranial tumors. We recently experienced a case of LWNH with intracranial lipoma of corpus callosum. We report this case with a brief review of the related literature.

Key Words: Intracranial lipoma, Linear and whorled nevoid hypermelanosis