A Case of Neurocutaneous Giant Melanosis Associated with Dandy-Walker Syndrome.

Hong,  Su Young; Ban,  Ji Eun; Rhu,  Jae Ho; Choi,  Sun Seob; Hwang,  Kyu Geun

Search: J Korean Child Neurol Soc Search

CLOSE

Case Report

Journal of the Korean Child Neurology Society 2001;9(1):171-177.
Published online May 30, 2001.

A Case of Neurocutaneous Giant Melanosis Associated with Dandy-Walker Syndrome.

Su Young Hong, Ji Eun Ban, Jae Ho Rhu, Sun Seob Choi, Kyu Geun Hwang

¹Department of Pediatrics, College of Medicine, Dong-A University, Pusan, Korea.
²Department of Diagnostic Radiology, College of Medicine, Dong-A University, Pusan, Korea.

Abstract

Neurocutaneous melanosis is a rare congenital phacomatosis, characterized by the presence of multiple pigmented skin nevi at birth. Meningeal melanosis tending to become malignant and seizure. Dandy-Walker syndrome is a developmental disorder of brain characterized by cystic dilatation of the fourth ventricle and agenesis or hypoplasia of the cerebellar vermis. We studied a case of Dandy-Walker syndrome with neurocutaneous giant melanosis in a 3 years old boy.

Key Words: Neurocutaneous giant melanosis, Dandy-Walker syndrome

TOOLS

PDF Links
Full text via DOI
Cited

Cited

export Copy Format

Close

Share :

METRICS

1,614 View
6 Download

Related articles in Ann Child Neurol

Two Cases of Norovirus Gastroenteritis Associated with Severe Neurologic Complications2023 January;31(1)

A Case of Mollaret's Meningitis Associated with Benign Pineal Cyst.2004 November;12(2)

A Case of Basal Ganglia Infarct Associated with SLE.2004 November;12(2)

A Case of Valproic Acid Associated with Acute Pancreatitis.2005 May;13(1)

A Case of Neurocutaneous Melanosis in a Child with Congenital Giant Nevi.2005 November;13(2)

Editorial Office: 372, Hangang-daero, Yongsan-gu, Seoul 04323, Republic of Korea 703, Building A, Centreville Asterium Seoul
Tel: +82-2-2138-3303 Fax: +82-2-743-3455 E-mail: editor@annchildneurol.org